Leber’s congenital amaurosis. Case report

Contenido principal del artículo

Elizabeth Quintino Cintora
Patricia Marcela López Morales
Vicente Mendoza Rosas

Resumen

Leber’s congenital amaurosis is an heterogeneous and genetic clinical disorder characterized by severe loss of vision at birth. It accounts for 10 to 18% of congenital blindness cases. Some patients exhibit solely retinal blindness and show evidence of multi-systemic involvement. The presentation of this case includes bibliographic review of the subject, presentation of a clinical case and description of the importance of stomatologic handling of these patients. Knowledge and understanding of the disease as well as treatment sequels are paramount.

Detalles del artículo

Cómo citar
Quintino Cintora, E., López Morales, P. M., & Mendoza Rosas, V. (2019). Leber’s congenital amaurosis. Case report. Revista Odontológica Mexicana Órgano Oficial De La Facultad De Odontología UNAM, 18(1). https://doi.org/10.22201/fo.1870199xp.2014.18.1 ING.69530
Biografía del autor/a

Elizabeth Quintino Cintora

Coordinación de publicaciones.

Editora de la Revista Ódontológica Mexicana. Órgano Oficial de la Facultad de Odontología, UNAM.