Osteogenic mandibular distraction in Nager’s Syndrome. Case report

Resumen

Osteogenic distraction is used nowadays for tissuelengtheningdue to the bone formation that occurs during the progressive segment separation after corticotomy, being very useful in dentofacial anomalies, especially in severe hypoplasia. We present the case report of a patient with Nager’s syndrome, acrofacial dysostosis of the preaxial type, severe mandibular hypoplasia and oligodonthia who was treated by means of distraction osteogenesiswith ramus osteotomies to lengthen the mandible. He was treated with a Spring Bite-type orthopaedic appliance after the osteotomies. We conclude that treatment with mandibular distraction should be comprehensive and supported with the use of miofuncional advices.

Key words: Nager’s syndrome, postaxial acrofacial dysostosis, mandibular distraction, mandibular hypoplasia and oligodonthia.